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ea0099p5 | Adrenal and Cardiovascular Endocrinology | ECE2024

A case of a composite pheochromocytoma with a spindle cell sarcoma exhibiting aggressive behavior

Venetsanaki Vasiliki , Sfakiotaki Maria , Kuo Mickey J. M. , Syntzanaki Eleni-Konstantina , Sertedaki Amalia , Papanastasiou Labrini , Fountas Athanasios , Zografos Georgios , Patel Mayank , Choreftaki Theodosia , Kyriakopoulos Georgios , Pacak Karel , Xekouki Paraskevi

Introduction: Pheochromocytomas (PHEOs) are rare catecholamine-producing tumors with metastatic potential. Composite PHEOs are rare (3% of adrenal tumors) including components other than adrenal chromaffin cells. We report a case of a rare composite neoplasm with a very rapid disease progression.Case report: A 57-year-old male was referred to the Endocrinology Department for investigation of a retroperitoneal mass. He presented with nonspecific symptoms ...